$148.00/50µL $248.00/100µL
| 50 µL | $148.00 |
| 100 µL | $248.00 |
| Product name: | ACADL rabbit pAb |
| Reactivity: | Human; Mouse;Rat |
| Source: | Rabbit |
| Dilutions: | WB 1:500-2000 |
| Immunogen: | Synthesized peptide derived from human ACADL AA range: 258-308 |
| Storage: | -20°C/1 year |
| Clonality: | Polyclonal |
| Isotype: | IgG |
| Concentration: | 1 mg/ml |
| Molecular Weight: | 47kD |
| GeneID: | 33 |
| Human Swiss-Prot No: | P28330 |
| Cellular localization: | Mitochondrion matrix . |
| Background: | The protein encoded by this gene belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia. [provided by RefSeq, Jul 2008], |