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AASS rabbit pAb
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ES1560
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50 µL $148.00
100 µL $248.00
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Overview

Product name: AASS rabbit pAb
Reactivity: Human;Rat;Mouse;
Alternative Names: AASS; Alpha-aminoadipic semialdehyde synthase; mitochondrial; LKR/SDH
Source: Rabbit
Dilutions: Western Blot: 1/500 - 1/2000. ELISA: 1/10000. Not yet tested in other applications.
Immunogen: The antiserum was produced against synthesized peptide derived from human AASS. AA range:251-300
Storage: -20°C/1 year
Clonality: Polyclonal
Isotype: IgG
Concentration: 1 mg/ml
Observed Band: 102kD
GeneID: 10157
Human Swiss-Prot No: Q9UDR5
Cellular localization: Mitochondrion .
Background: This gene encodes a bifunctional enzyme that catalyzes the first two steps in the mammalian lysine degradation pathway. The N-terminal and the C-terminal portions of this enzyme contain lysine-ketoglutarate reductase and saccharopine dehydrogenase activity, respectively, resulting in the conversion of lysine to alpha-aminoadipic semialdehyde. Mutations in this gene are associated with familial hyperlysinemia. [provided by RefSeq, Jul 2008],