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LYAG rabbit pAb
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ES15073
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50 µL $148.00
100 µL $248.00
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Overview

Product name: LYAG rabbit pAb
Reactivity: Human; Mouse;Rat
Alternative Names: Lysosomal alpha-glucosidase (EC 3.2.1.20) (Acid maltase) (Aglucosidase alfa) [Cleaved into: 76 kDa lysosomal alpha-glucosidase; 70 kDa lysosomal alpha-glucosidase]
Source: Rabbit
Dilutions: WB 1:500-2000
Immunogen: Synthesized peptide derived from human LYAG AA range: 432-482
Storage: -20°C/1 year
Clonality: Polyclonal
Isotype: IgG
Concentration: 1 mg/ml
Observed Band: 105kD
GeneID: 2548
Human Swiss-Prot No: P10253
Cellular localization: Lysosome . Lysosome membrane .
Background: This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016],